Single ventricle
Single ventricle is a rare congenital heart defect, which constitutes just over 1% of congenital cardiovascular diseases.[1] The single functional ventricle could be morphologically right or left with the second ventricle usually hypoplastic and/or insufficiently functional. Therefore, there are several subtypes of the disease, depending on which ventricle is underdeveloped.
- Single ventricle with functional left ventricle:
- Pulmonal atresia
- Tricuspidal atresia
- Double inlet left ventricle
- Double outlet left ventricle
- Single ventricle with functional right ventricle:
- Hypoplastic left heart syndrome
- Double inlet right ventricle
- Double outlet right ventricle
- Single ventricle heterotaxy syndrome is also included to this category.[2]
- ^ Steinberger, Eileen K.; Ferencz, Charlotte; Loffredo, Christopher A. (March 2002). "Infants with single ventricle: a population-based epidemiological study". Teratology. 65 (3): 106–115. doi:10.1002/tera.10017. ISSN 0040-3709. PMID 11877773.
- ^ Khairy, Paul; Poirier, Nancy; Mercier, Lise-Andrée (2007-02-13). "Univentricular Heart". Circulation. 115 (6): 800–812. doi:10.1161/circulationaha.105.592378. ISSN 0009-7322. PMID 17296869. S2CID 33669345.